Description
Dietary food intended for special medical purposes, for the dietary treatment of phenylketonuria in children from the 6th month of life onwards, in adults with confirmed phenylketonuria and/or hyperphenylalaninemia and in maternal phenylketonuria.
Phenylalanine-free amino acid blend supplemented with vitamins, minerals, selenium, taurine and carnitine.

Ingredients
Sucrose, corn starch, L-lysine-L-aspartate, modified corn starch, L-leucine, L-tyrosine, glycine, L-valine, L-glutamine, L-arginine-L-aspartate, L-proline, L-threonine, L-isoleucine, tricalcium phosphate, L-serine, calcium glycerophosphate, sodium citrate, L-alanine, L-histidine, potassium citrate, L-cystine, L-arginine, magnesium hydrogen phosphate, L-tryptophan, L-methionine, choline bitartrate, maltodextrin (from potato), sodium chloride, taurine, zinc gluconate, L-carnitine-L-tartrate, L-ascorbic acid (vitamin C), ferrous sulfate, DL-alpha tocopheryl acetate (vitamin E), manganese gluconate, nicotinamide (niacin), cholecalciferol (vitamin D), cupric gluconate, calcium D-pantothenate, retinyl acetate (vitamin A), potassium iodide, riboflavin (vitamin B2), pyridoxine hydrochloride (vitamin B6), thiamine hydrochloride (vitamin B1), phylloquinone (vitamin K), folic acid (pteroylmonoglutamic acid), sodium molybdate, sodium selenite, chromium (III) chloride, D-biotin, cyanocobalamin (vitamin B12).

Nutritional characteristics

Nutritional information	per 100 g of powder	per sachet (24 g)
Energy value	1,388 kJ / 327 kcal	333 kJ / 78 kcal
Protein equivalents	42 g	10 g
Carbohydrates of which sugars	39.4 g 25.5 g	9.5 g 6.1 g
Fats of which saturated	0 g 0 g	0 g 0 g
Salt	0.98 g	0.23 g
Choline	279 mg	67 mg
Vitamin C	63 mg	15 mg
Niacin	14 mg	3.4 mg
Vitamin E (α-TE)	9 mg	2.2 mg
Pantothenic acid	5 mg	1.2 mg
Vitamin B2	1.2 mg	0.29 mg
Vitamin B6	1.1 mg	0.26 mg
Vitamin B1	1 mg	0.24 mg
Vitamin A (RE)	600 mcg	144 mcg
Folic acid	208 mcg	49.9 mcg
Vitamin K	41 mcg	9.8 mcg
Biotin	25 mcg	6 mcg
Vitamin D	14.6 mcg	3.5 mcg
Vitamin B12	2 mcg	0.48 mcg
Soccer	1083 mg	260 mg
Potassium	938 mg	225 mg
Phosphorus	825 mg	198 mg
Chlorine	583 mg	140 mg
Sodium	379 mg	91 mg
Magnesium	167 mg	40 mg
Iron	14 mg	3.4 mg
Zinc	11 mg	2.6 mg
Manganese	1.7 mg	0.41 mg
Copper	0.8 mg	0.19 mg
Iodine	138 mcg	33.1 mcg
Chrome	71 mcg	17 mcg
Molybdenum	50 mcg	12 mcg
Selenium	35 mcg	8.4 mcg
Leucine	4.7 g	1.1 g
Aspartic acid	4.6 g	1.1 g
Glycine	4.6 g	1.1 g
Tyrosine	4.6 g	1.1 g
Glutamine	3.6 g	0.9 g
Valine	3.6 g	0.9 g
Proline	3.3 g	0.8 g
Lysine	3.3 g	0.8 g
Threonine	3.2 g	0.8 g
Isoleucine	3.1 g	0.7 g
Arginine	2.9 g	0.7 g
Serina	2 g	0.5 g
Alanine	1.8 g	0.4 g
Histidine	1.8 g	0.4 g
Cystine	1.2 g	0.3 g
Tryptophan	1 g	0.2 g
Methionine	0.9 g	0.2 g
Taurine	92 mg	22 mg
Carnitine	46 mg	11 mg

How to use
Dosage : as prescribed by the doctor, taking into account the patient's age, body weight, degree of phenylalaninemia and the patient's clinical conditions.
To obtain a gel
1) Pour the contents of one sachet into a glass. If desired, flavor to taste.
2) Add about 30 ml of cold water. Mix well for about 10 seconds.
3) To obtain a creamy gel, let it sit for about 2 minutes. The reconstituted gel can be taken as is with a teaspoon or mixed with other permitted foods. For best results, whenever possible, it should be prepared and consumed immediately. If necessary, the reconstituted product can be refrigerated for 24 hours and stirred well before use.
To get a drink.
1) Pour the contents of one sachet into a glass. If desired, flavor to taste.
2) Add about 80 ml of cold water. Mix well for about 10 seconds.
3) Drink immediately.
Once opened, the powder contained in a sachet should be consumed entirely. Any excess should be refrigerated and used within 24 hours.

Warnings
It must be used under strict medical supervision by people with known phenylketonuria.
This product cannot be the sole source of nutrition. The diet must be supplemented with natural proteins, water, and other nutrients in the prescribed amounts to provide phenylalanine, fluids, and other necessary nutrients.
Not to be used intravenously.
Keep out of reach of children under 3 years of age.

Conservation
Store in a cool, dry place, away from light and direct sources of heat.
Shelf life in unopened packaging: 24 months.

Format
720 g box – 30 24 g bags.

Code 3020